Case Report: Cardiovertor-Defibrillator Implantation in an Isolated PLSVC with Hypertrophic Cardiomyopathy
DOI:
https://doi.org/10.12970/2311-052X.2014.02.02.2Keywords:
Persistent left superior vena cava, isolated superior vena cava, absent right superior vena cava, combined superior vena cava, Hypertrophic cardiomyopathy, Cardioverter-defibrillator, Anomalies of superior vena cava.Abstract
Persistent Left Superior Vena Cava (PLSVC) has an estimated incidence of 0.2-0.8% in the general population and 3-10% in patients with known congenital heart disease [1]. A rare anatomic variation of LSVC occurs in up to 0.13% of otherwise normal individuals where both brachiocephalic venous systems drain into a persistent LSVC [1]. We describe a patient with hypertrophic cardiomyopathy (HCM) and malignant ventricular arrhythmias in whom this rare malformation was discovered at the time of implantable cardioverter–defibrillator (ICD) implant.References
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