Now you see the drum, now you don’t: a rare case of conductive hearing loss in a child
DOI:
https://doi.org/10.12970/2311-1917.2017.05.01Keywords:
Temporal bone, fibrous dysplasia, craniofacial, auditory canal, hearing loss.Abstract
Introduction: Fibrous dysplasia is a benign disease of the bones, which affects the differentiation and maturation of osteoblasts. Fibrous dysplasia can affect the craniofacial bones, which can be asymptomatic or present with symptoms commonly found in an ENT outpatient clinic.
Method: We present an unusual case of temporal bone fibrous dysplasia. This is used as a platform to discuss craniofacial fibrous dysplasia further and the investigations and management.
Results: Other cases have been reported on temporal bone fibrous dysplasia, but our case is unique in the presentation. Gold-standard diagnosis for craniofacial fibrous dysplasia is by histopathological sampling, although computerised-tomography imaging can be used to diagnose fibrous dysplasia if a biopsy cannot be sought.
Conclusion: Fibrous dysplasia of the temporal bones is uncommon. Many cases from other series are found incidentally from radiology reports.
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