Primary Cutaneous Ewing´s Sarcoma: A Rare and Deadly Tumor. Case Report and Literature Review
DOI:
https://doi.org/10.12970/2310-998X.2017.05.04Keywords:
Ewing´s sarcoma, cutaneous, extra-skeletal.Abstract
Introduction: Ewing´s Sarcoma (ES) is a neuroectodermic tumor that rarely occurs on skin. In 85% presents in bones, and another 15% in extraskeletal tissue. It is the second most common bone cancer in children. ES has an incidence of one case per million per year, and the average age of presentation is 15 year-old. Extraskeletal ES has low frequency, and has been described at the para-spinal region, thoracic wall and lower extremities.
Objective: To report a low frequency clinical case, with controversies in its classification.
Clinical Case: A 79 year-old male with previous frontal basal cell carcinoma (BCC) history, assists to our department because of one-month evolution nasal tumor, which appeared the novo. The lesion was approximately 18 millimeters in diameter, with a 10 millimeters base, erythematous, firm to palpation. The histopathology demonstrated an Ewing´s sarcoma. The tumor had an extremely aggressive behavior, presenting local metastasis prematurely.
Conclusion: Thereby, we present a case of cutaneous Ewing´s sarcoma in an older adult with an aggressive behavior. The superficial cases of Extraskeletal Ewing´s sarcoma are exceedingly rare, and the majority is reported as a unique and small firm mass.
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