Incontinetia Pigmenti in Males: Report of 2 Cases and Literature Review
DOI:
https://doi.org/10.12970/2310-998X.2017.05.01Keywords:
Incontinentia pigmenti, male, newborn, NEMO.Abstract
Incontinentia Pigmenti (IP) is a rare X-linked genodermatosis.
Papules, vesicles and changes in pigmentation following the Blaschko lines during neonate period are distinctive with only few male cases reported in the literature. We report two cases of IP in males. One of the cases was associated with mild peripheral eosinophilia, which is characteristic. No extra-cutaneous manifestations were noted in neither of the cases. This report aims to be a reminder for clinicians to consider IP in newborns presenting with linear vesicles or papules, discuss the differential diagnosis and a brief review of the literature.
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