Case Report: Cardiovertor-Defibrillator Implantation in an Isolated PLSVC with Hypertrophic Cardiomyopathy Pages 68-69

Shivang Shah1, Rosy Thachil2, Shenil Shah3, Navdeep Mann4 and Fabio Leonelli5

1Department of Cardiology, University of South Florida, Tampa, FL, USA; 2Department of Internal Medicine, Drexel University College of Medicine, Philadelphia, PA, USA; 3Department of Internal Medicine, University Hospitals Case Medical Center, Cleveland, OH, USA; 4Heart Center, Huntsville, AL, USA; 5Department of Cardiology and Electrophysiology, James A. Haley VA Hospital, Tampa, FL, USA

DOI: http://dx.doi.org/10.12970/2311-052X.2014.02.02.2

Abstract: Persistent Left Superior Vena Cava (PLSVC) has an estimated incidence of 0.2-0.8% in the general population and 3-10% in patients with known congenital heart disease [1]. A rare anatomic variation of LSVC occurs in up to 0.13% of otherwise normal individuals where both brachiocephalic venous systems drain into a persistent LSVC [1]. We describe a patient with hypertrophic cardiomyopathy (HCM) and malignant ventricular arrhythmias in whom this rare malformation was discovered at the time of implantable cardioverter–defibrillator (ICD) implant.

Keywords: Persistent left superior vena cava, isolated superior vena cava, absent right superior vena cava, combined superior vena cava, Hypertrophic cardiomyopathy, Cardioverter-defibrillator, Anomalies of superior vena cava. Read more